Intramedullary cavernous angioma of the spinal cord in a pediatric case with multiple cerebral cavernomas and familial occurrence case report and review of the literature
Küçük Resim Yok
Tarih
2010
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Erişim Hakkı
info:eu-repo/semantics/openAccess
Özet
Manyetik rezonans incelemesi (MRI) tekniklerinin gelişmesi sonrasında literatürde bildirilen intramedüller kavernoz anjiomlu (ImCA) vaka sayısında büyük artış olmuştur. Literatürdeki erişkin ve çocuk ImCA vakaları incelendiğinde, çok sayıdaki yetişkin vakanın yanında, sadece 18 pediatrik vaka bildirildiği görülmektedir. Bu çalışmanın amacı, 19. pediatrik vakayı bildirmek ve literatür gözden geçirmesininde yardımıyla hastaların klinik prezentasyonu, seyri, yönetimi ve sonuçlarının tartışılmasıdır. Bu vakanın bir diğer özelliği ailesel geçiş göstermesi ve serebral hemisferlerde üç ayrı lezyonunda bulunmasıdır. Spinal lezyonun cerrahi ile tam olarak çıkarılması başarılmış ve radyolojik olarakda bu durum kanıtlanmıştır. Takip radyolojik incelemeleri ve nörolojik muayeneleri yapılmış ve cerrahiden sonraki izlemi sırasında herhangi bir komplikasyonla karşılaşılmamıştır.
The review of data available in the literature has shown that there has been a gradual increase in the number of reported cases of intramedullary cavernous angioma (ImCA) since the advent of Magnetic Resonance Imagining (MRI). However, a comparison between the number of studies on adult and pediatric ImCA cases reveals that the total number of pediatric ImCA cases reported to date is only 18 - quite smaller than the former. The purpose of this study is to present an outline of ImCA in pediatric age group; its clinical presentation, course, management and outcome and to report the 19th pediatric case with an ImCA. Another important point about the present case is the three intracerebral lesions she had and the familial pattern existed. A complete removal of the lesion was accomplished as demonstrated by postoperative MRI studies. At the follow-up examination, a spine and cerebral MRI was completed and it was clear that no postoperative complication occurred after surgery.
The review of data available in the literature has shown that there has been a gradual increase in the number of reported cases of intramedullary cavernous angioma (ImCA) since the advent of Magnetic Resonance Imagining (MRI). However, a comparison between the number of studies on adult and pediatric ImCA cases reveals that the total number of pediatric ImCA cases reported to date is only 18 - quite smaller than the former. The purpose of this study is to present an outline of ImCA in pediatric age group; its clinical presentation, course, management and outcome and to report the 19th pediatric case with an ImCA. Another important point about the present case is the three intracerebral lesions she had and the familial pattern existed. A complete removal of the lesion was accomplished as demonstrated by postoperative MRI studies. At the follow-up examination, a spine and cerebral MRI was completed and it was clear that no postoperative complication occurred after surgery.
Açıklama
Anahtar Kelimeler
Nörolojik Bilimler
Kaynak
Journal of Neurological Sciences (Turkish)
WoS Q Değeri
Scopus Q Değeri
Cilt
27
Sayı
3
