Rarer Components of a Rare Disease: Accessory Hemidiaphragm and Horseshoe Lung with Scimitar Syndrome: Two Case Reports

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Tarih

2024

Dergi Başlığı

Dergi ISSN

Cilt Başlığı

Yayıncı

Bentham Science Publishers

Erişim Hakkı

info:eu-repo/semantics/openAccess

Özet

Introduction: Scimitar syndrome is a rare developmental anomaly with an incidence of 2/100.000 births. Major components of this disease are partial anomalous pulmonary venous drainage, pulmonary hypoplasia, systemic arterialization of the right basal lung, and dextroposition of the heart. Horseshoe lung and accessory hemidiaphragm are two rarer components of this disease. Case Presentation: In this paper, horseshoe lung and accessory diaphragm associated with Scimitar syndrome have been reported in two cases. Conclusion: In conclusion, being aware of rare manifestations of rare diseases is important to fully describe the pathologic spectrum of the disease. This will assist in better management and decision-making process. © 2024 The Author(s).

Açıklama

Anahtar Kelimeler

Accessory hemidiaphragm, Case report, Horseshoe lung, Pulmonary hypoplasia, Pulmonary hypoplasia, Scimitar syndrome, Article, bronchus obstruction, case report, clinical article, computer assisted tomography, coughing, decision making, heart atrium septum defect, hemidiaphragm, horseshoe lung, human, inferior cava vein, lung vein drainage anomaly, physical examination, rare disease, right ventricular dilatation, scimitar syndrome, thorax radiography

Kaynak

Current Medical Imaging

WoS Q Değeri

Scopus Q Değeri

Q3

Cilt

20

Sayı

Künye