Chronic inflammatory demyelinating polyradiculopathy: an atypical pediatric case complicated with phrenic nerve palsy

Küçük Resim Yok

Tarih

2007

Dergi Başlığı

Dergi ISSN

Cilt Başlığı

Yayıncı

Turkish J Pediatrics

Erişim Hakkı

info:eu-repo/semantics/closedAccess

Özet

An atypical form of chronic inflammatory demyelinating polyneuropathy (CIDP) complicated with phrenic nerve palsy is presented with clinical and electrophysiologic features. A seven-year-old girl had initial presentation mimicking Guillain-Barre syndrome based on electrophysiologic characteristics. Between 7-11 years of age, she had five recurrences of subacute onset of weakness which usually developed over at least 2-4 months and progressed to loss of ambulation and to respiratory insufficiency. Radiologic examinations revealed unilateral phrenic nerve palsy associated with CIDP. Our patient demonstrated the rare association of CIDP and phrenic nerve palsy, resulting in diaphragmatic paralysis and respiratory failure.

Açıklama

Anahtar Kelimeler

chronic inflammatory demyelinating polyradiculopathy, phrenic nerve palsy, respiratory failure, EMG, MRI

Kaynak

Turkish Journal of Pediatrics

WoS Q Değeri

Q4

Scopus Q Değeri

Q3

Cilt

49

Sayı

2

Künye