Non-MEN Familial Endocrine Syndromes: Von Recklinghausen Disease, Von Hippel-Lindau Syndrome, Pheochromocytoma/Paraganglioma

This chapter briefly describes familial endocrine syndromes besides MEN, including hereditary pheochromocytoma or paragangliomas, von Hippel-Lindau syndrome, and neurofibromatosis type 1 (von Recklinghausen disease). The contents of this chapter include a summary of the most recent literature regarding the epidemiology and genetics, clinical presentations, diagnosis and indications for surgery, preoperative management and radiological studies, surgical techniques and approaches, postoperative follow-up, and prognosis for these syndromes. © Springer Nature Switzerland AG 2021.