Pseudo-Bartter Syndrome in Patients with Cystic Fibrosis and Clinical Features

Basit Öğe Kaydı
dc.contributor.authorOzaslan, Mehmet Mustafa
dc.contributor.authorSenol, Handan Duman
dc.contributor.authorBarlık, Meral
dc.contributor.authorCoksuer, Fevziye
dc.contributor.authorDindar, Bahar
dc.contributor.authorDemir, Esen
dc.contributor.authorGülen, Figen
dc.date.accessioned2024-08-25T18:52:15Z
dc.date.available2024-08-25T18:52:15Z
dc.date.issued2023
dc.departmentEge Üniversitesien_US
dc.description.abstractObjective: Pseudo-Bartter syndrome (PBS) is a complication of cystic fibrosis (CF) accompanied by electrolyte disorders. We aimed to compare the clinical features of patients diagnosed with CF with or without PBS in our clinic.Method: One hundred twenty-eight patients with the diagnosis CF data was recorded. Clinical features, diagnostic test results, colonization status, complications and genetic test results were compared in patients with and without PBS.Results: Totally 128 patients who were regularly followed diagnosis CF January 2017 and May 2022 and 18 of them (14%) developed PBS. Median age of CF diagnosis was significantly lower in patients with PBS (p<0.003). There was a significant difference between the two groups in terms of colonization. In the group with PBS, the chronic respiratory tract colonization was detected more. There were no significant differences for age, gender, weight, height, sweat test. The most common genetic mutation was c1521_1523delCTT (p. F508Del).Conclusion: PBS was the most common finding in our patients with CF. It may be exacerbated by the warm weather conditions in our country. It may be a clue for early diagnosis of CF.en_US
dc.identifier.doi10.4274/buchd.galenos.2023.4452
dc.identifier.endpage100en_US
dc.identifier.issn2822-4469
dc.identifier.issue2en_US
dc.identifier.startpage94en_US
dc.identifier.urihttps://doi.org/10.4274/buchd.galenos.2023.4452
dc.identifier.urihttps://hdl.handle.net/11454/102909
dc.identifier.volume13en_US
dc.identifier.wosWOS:001049222400003en_US
dc.identifier.wosqualityN/Aen_US
dc.indekslendigikaynakWeb of Scienceen_US
dc.language.isoenen_US
dc.publisherGalenos Publ Houseen_US
dc.relation.ispartofJournal of Dr Behcet Uz Childrens Hospitalen_US
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanıen_US
dc.rightsinfo:eu-repo/semantics/closedAccessen_US
dc.snmz20240825_Gen_US
dc.subjectCystic fibrosisen_US
dc.subjectPseudo-Bartter syndromeen_US
dc.subjectcomplicationsen_US
dc.titlePseudo-Bartter Syndrome in Patients with Cystic Fibrosis and Clinical Featuresen_US
dc.typeArticleen_US

Dosyalar

Koleksiyon

WoS İndeksli Yayınlar Koleksiyonu