Early and mid-term outcomes after surgical repair of congenital supravalvular aortic stenosis with the Doty technique

Küçük Resim Yok

Tarih

2018

Dergi Başlığı

Dergi ISSN

Cilt Başlığı

Yayıncı

Turkish Soc Cardiology

Erişim Hakkı

info:eu-repo/semantics/openAccess

Özet

Objective: The aim of this study was to evaluate the efficacy and safety of the Doty surgical approach in pediatric patients with congenital supravalvular aortic stenosis (SVAS) by examining early and mid-term outcomes. Methods: Surgical repair using the Doty technique was performed in a total of 10 pediatric patients with SVAS between January 2005 and July 2015 at this clinic. These patients were evaluated retrospectively. Demographic characteristics, echocardiographic findings, and clinical outcomes were analyzed. Results: The mean patient age was 4.8 +/- 3.9 years. Williams-Beuren syndrome was diagnosed in 4 of the patients. Early mortality was observed in 1 patient with diffuse SVAS. At the final follow-up (mean follow-up: 3.7 +/- 1.2 years; range: 6-61 months), echocardiograms revealed a mean pressure gradient of 14 +/- 4.2 mmHg. Two patients displayed minimal aortic insufficiency during the follow-up period. No reoperation or reintervention was required. Conclusion: The Doty technique is an anatomically and technically effective surgical approach to treating SVAS.

Açıklama

Anahtar Kelimeler

Doty technique, supravalvular aortic stenosis, Williams-Beuren syndrome

Kaynak

Turk Kardiyoloji Dernegi Arsivi-Archives of the Turkish Society of Cardiology

WoS Q Değeri

N/A

Scopus Q Değeri

Cilt

46

Sayı

5

Künye