Early and mid-term outcomes after surgical repair of congenital supravalvular aortic stenosis with the Doty technique
Küçük Resim Yok
Tarih
2018
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Turkish Soc Cardiology
Erişim Hakkı
info:eu-repo/semantics/openAccess
Özet
Objective: The aim of this study was to evaluate the efficacy and safety of the Doty surgical approach in pediatric patients with congenital supravalvular aortic stenosis (SVAS) by examining early and mid-term outcomes. Methods: Surgical repair using the Doty technique was performed in a total of 10 pediatric patients with SVAS between January 2005 and July 2015 at this clinic. These patients were evaluated retrospectively. Demographic characteristics, echocardiographic findings, and clinical outcomes were analyzed. Results: The mean patient age was 4.8 +/- 3.9 years. Williams-Beuren syndrome was diagnosed in 4 of the patients. Early mortality was observed in 1 patient with diffuse SVAS. At the final follow-up (mean follow-up: 3.7 +/- 1.2 years; range: 6-61 months), echocardiograms revealed a mean pressure gradient of 14 +/- 4.2 mmHg. Two patients displayed minimal aortic insufficiency during the follow-up period. No reoperation or reintervention was required. Conclusion: The Doty technique is an anatomically and technically effective surgical approach to treating SVAS.
Açıklama
Anahtar Kelimeler
Doty technique, supravalvular aortic stenosis, Williams-Beuren syndrome
Kaynak
Turk Kardiyoloji Dernegi Arsivi-Archives of the Turkish Society of Cardiology
WoS Q Değeri
N/A
Scopus Q Değeri
Cilt
46
Sayı
5