Classical triad in pulmonary arteriovenous malformation: Clubbing, cyanosis and policytemia [Pulmoner arteriyovenöz Malformasyonda klasik triad: Çomak parmak, siyanoz ve polisitemi]

Pulmonary arteriovenous malformations (PAVM) are generally congenital lesions that results from an abnormal capillary development. Lesions can be presented as an isolated single anomaly, or may be multiple when accompanying with autosomal dominant hereditary hemorrhagic telangiectasia (Rendu-Osler-Weber Syndrome; ROWS). These cases may be asymptomatic, but exertional dyspnea, palpitations and easy fatigability may also be seen. The classic radiological appearance is a round, well-circumscribed lesions. Computed tomography of thorax and angiography are also useful for diagnosis. Herein, we present 2 and 13 years old girls with the diagnosis of PAVM with clubbing and cyanosis. © The Journal of Current Pediatrics, published by Galenos Publishing.