Successful treatment of congenital systemic juvenile xanthogranulomatosis with pulmonary involvement
Küçük Resim Yok
Tarih
2021
Yazarlar
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Wiley
Erişim Hakkı
info:eu-repo/semantics/closedAccess
Özet
Juvenile xanthogranuloma (JXG) is a common form of non-Langerhans cell histiocytosis, which usually presents with spontaneously regressing skin lesions. Systemic involvement is rare and mostly seen in patients with multiple skin nodules. It can spontaneously regress, but sometimes systemic involvement can cause life-threatening symptoms and can be fatal. Herein, we report a case of congenital systemic JXG with multiple skin nodules, soft tissue and pulmonary involvement. She was successfully treated with chemotherapy according to Langerhans cell histiocytosis treatment protocol IV of the Histiocyte Society (LCH-IV).
Açıklama
Anahtar Kelimeler
congenital juvenile xanthogranuloma, lung metastases, systemic juvenile xanthogranuloma, Disease, Tumor
Kaynak
Pediatric Dermatology
WoS Q Değeri
Q3
Scopus Q Değeri
Q2
Cilt
38
Sayı
4
