Evaluation of Supravalvular Changes in Aortic ID Gradient Following Inverted Y-Patch Repair

Küçük Resim Yok

Tarih

2020

Dergi Başlığı

Dergi ISSN

Cilt Başlığı

Yayıncı

Erişim Hakkı

info:eu-repo/semantics/openAccess

Özet

Objective: This study presents our single-institute experience regarding the patients who underwent sur-gical correction via inverted Y-patch repair with the diagnosis of supravalvular aortic stenosis. Method: A total of 16 patients who underwent inverted Y-patch (Doty) repair in our center between 2005 and 2019 were retrospectively analyzed. Complications, supravalvular residual gradient measurements, causes of re-operation were evaluated. Results: Patient population consisted of 9 males, 7 females with an overall mean age of 41.18±16.14 months (range: 4 months to 19 years). Eight (50%) patients were diagnosed with Williams-Beuren syndro-me and 3 (18.7%) with bicuspid aortic valve. Three (18.7%) patients had undergone simultaneous subaor-tic membrane resection and pulmonary patch plasty was performed in 2 (12.5%) patients. There was one (6.7%) inhospital death and no mortality was observed during follow-up. The mean follow-up time was 5.25±3.37 years. During this period, 2 (12.5%) patients required pulmonary balloon dilatation and one patient repeated Doty repair and aortic valve commissurotomy two years after the initial surgery. Thereafter the same patient needed aortic homograft valve replacement and Doty repair for the third time due to severe aortic insufficiency and suprvalvular aortic stenosis.Conclusion: Inverted Y-patch repair provides satisfactory results, acceptable reoperation risk, and good overall survival.

Açıklama

Anahtar Kelimeler

Kaynak

İzmir Dr. Behçet Uz Çocuk Hastanesi Dergisi

WoS Q Değeri

Scopus Q Değeri

Cilt

10

Sayı

2

Künye